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History and Diagnosis

  • Colin G. Barnes
  • Yusuf Yazici
Chapter

Abstract

Behçet syndrome, named after Hulusi Behçet, Professor of Dermatology in Istanbul who described the “triple symptom complex” in 1937, is a multisystem, immunologically medicated vasculopathy. The principal clinical features are orogenital aphthous ulceration, uveitis with or without hypopyon and retinal vasculitis, and skin lesions including erythema nodosum and acneiform pustules. Inflammatory arthritis, arterial and venous occlusion and arterial aneurysms, and gastrointestinal and neurological lesions also occur.

Keywords

Aphthous ulceration Behçet’s disease Behcet’s syndrome Classification Diagnostic criteria Pathergy Vasculitis Vasculopathy 

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Copyright information

© Springer Nature Switzerland AG 2020

Authors and Affiliations

  • Colin G. Barnes
    • 1
    • 2
    • 3
    • 4
  • Yusuf Yazici
    • 5
  1. 1.(Formerly of the) Department of RheumatologyThe Royal London HospitalLondonUK
  2. 2.(Formerly of the) Queen Mary College, University of LondonLondonUK
  3. 3.Little HoopernChagfordUK
  4. 4.European League Against RheumatismZürichSwitzerland
  5. 5.School of MedicineNew York UniversityNew YorkUSA

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