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Red Peeling

  • Ziying V. Lim
  • Emily Y. Gan
Chapter

Abstract

Netherton syndrome is a rare autosomal recessive disorder presenting with a generalized ichthyosiform erythroderma, characteristic hair shaft abnormality and allergic manifestations

Netherton syndrome is caused by germline mutations in the SPINK5 gene

Management of Netherton syndrome should be multidisciplinary, involving fluid and electrolyte correction, conscientious skin care with frequent application of emollients, prompt treatment of cutaneous and systemic infective complications, and nutritional support

Keywords

Netherton syndrome Ichthyosiform erythroderma SPINK5 

References

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Copyright information

© Springer Nature Switzerland AG 2019

Authors and Affiliations

  • Ziying V. Lim
    • 1
  • Emily Y. Gan
    • 1
    • 2
  1. 1.National Skin CentreSingaporeSingapore
  2. 2.Dermatology Service, KK Women’s and Children’s HospitalSingaporeSingapore

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