Extrapulmonary Respiratory Diseases
Restrictive lung diseases (RLDs) are disease processes which limit expansion of the respiratory system resulting in a reduction in lung volumes when measured by pulmonary function tests (PFTs). Extrapulmonary lung diseases cause respiratory muscle weakness, significant skeletal deformity or scarring of the pleural space can result in reduced lung volumes due an inability to expand the chest wall and therefore the lungs. These physiologic abnormalities can lead to increased perioperative risks but these can be mitigated with a careful preoperative evaluation and the use of noninvasive ventilation support and cough support with mechanical insufflation–exsufflation (MI-E or CoughAssist™) postoperatively.
KeywordsExtrapulmonary lung disease Restrictive lung disease Perioperative care
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