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Exercise Testing in Pediatric Dilated Cardiomyopathy

  • Irene D. LytriviEmail author
  • T. P. Singh
Chapter

Abstract

Dilated cardiomyopathy (DCM) is the most common cardiomyopathy in children, and its hallmark is left ventricular (LV) dilation and systolic dysfunction. Impairment of exercise performance in children with DCM is due to a combination of inadequate tissue O2 delivery resulting from impaired heart rate and stroke volume increase with exercise and abnormalities in distribution or impedance to flow in pulmonary and peripheral circulations and of the skeletal muscle. Formal assessment of exercise performance is useful in identifying limitations and eliciting the mechanism of limitations in children with moderate and severe LV dysfunction and has a potential role in risk stratification of those with severe LV dysfunction.

Keywords

Dilated cardiomyopathy Cardiopulmonary exercise testing Children Prognosis 6-minute walk test 

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Copyright information

© Springer Nature Switzerland AG 2019

Authors and Affiliations

  1. 1.Department of PediatricsColumbia University Medical CollegeNew YorkUSA
  2. 2.Program for Pediatric Cardiomyopathy, Heart Failure and Transplantation, Division of Pediatric CardiologyColumbia Presbyterian HospitalNew YorkUSA
  3. 3.Department of PediatricsHarvard Medical SchoolBostonUSA
  4. 4.Heart Failure/Transplant Service, Department of CardiologyBoston Children’s HospitalBostonUSA

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