Congenital Absence of Pericardium

  • Atooshe Rohani
Part of the Clinical Cases in Cardiology book series (CCC)


Congenital absence of the pericardium is a rare abnormality, most often asymptomatic but, patient may present with chest pain. This patient is an 18 year old young man who referred for bicuspid aortic valve screening and found to have congenital absence of the pericardium.


Congenital absence of the pericardium TTE 

Supplementary material

Movie 55.1

Para sternal long axis shows tear dropped heart, RV appears enlarged with elongated both atrium (AVI 7195 kb)


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Copyright information

© Springer Nature Switzerland AG 2019

Authors and Affiliations

  • Atooshe Rohani
    • 1
  1. 1.Northern Ontario School of MedicineThunder BayCanada

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