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Tricuspid Valve: Congenital Abnormalities and Stenosis

  • Pei-Ni JoneEmail author
  • Shelby Kutty
Chapter

Abstract

Three-dimensional echocardiography (3DE) has incremental diagnostic value over two-dimensional echocardiography in the evaluation of the tricuspid valve. 3DE provides en face view of all leaflets of the tricuspid valve. The understanding of tricuspid valve leaflet morphology and mechanisms of valvular regurgitation from 3DE provides valuable insights into tricuspid valve function, and assists in the planning for surgical interventions. Congenital abnormalities of the tricuspid valve and illustrative clinical cases are presented in this chapter.

Keywords

Three-dimensional echocardiography Tricuspid valve Tricuspid valve dysplasia Ebstein anomaly Tricuspid valve prolapse Functional abnormalities of the tricuspid valve Tricuspid valve in corrected transposition Tricuspid valve stenosis Tricuspid regurgitation. 

Supplementary material

Video 19.1

Normal tricuspid valve imaged by transesophageal echocardiography from a right atrial perspective (AVI 325 kb)

Video 19.2a

Thickened and dysplastic tricuspid valve leaflets from the apical four chamber view, with the heart rotated and cropped from behind (AVI 4871 kb)

Video 19.2b

This illustrates evaluation of thickened dysplastic tricuspid valve leaflets from the right ventricle up after cropping from a transthoracic three-dimensional full volume (AVI 4042 kb)

Video 19.3a

The tricuspid valve in Ebstein anomaly from a right ventricular perspective. Note the anterior leaflet displacement anteriorly into the right ventricular outflow tract (AVI 1871 kb)

Video 19.3b

Parasternal short axis view in Ebstein anomaly demonstrating the failure of delamination of the septal leaflet and the inability of tricuspid valve to coapt (AVI 1486 kb)

Video 19.4

Right atrial view of moderate to severe tricuspid regurgitation in Ebstein anomaly (AVI 3069 kb)

Video 19.5

Right ventricular view of the Ebstein tricuspid valve and the inability of leaflets to coapt (AVI 11248 kb)

Video 19.6a

Right atrial view of the prolapsing cleft tricuspid valve into the right atrium (AVI 10802 kb)

Video 19.6b

Transesophageal echocardiogram in the midesophageal view demonstrates the prolapse of the tricuspid valve into the right atrium (AVI 1000 kb)

Video 19.7

Severe tricuspid regurgitation of the cleft tricuspid valve with prolapse (AVI 868 kb)

Video 19.8a

This is prolapse of the anterior leaflet of the tricuspid valve demonstrated with three-dimensional transesophageal echocardiography in a patient with corrected transposition of the great arteries (AVI 2212 kb)

Video 19.8b

Straddling of the tricuspid valve shown by transthoracic subcostal three-dimensional echocardiography in a patient with corrected transposition of the great arteries (AVI 4420 kb)

Video 19.9

Three-dimensional transesophageal echocardiography in a stenotic bioprosthetic valve from the right atrial perspective (AVI 75902 kb)

Video 19.10

Three-dimensional transesophageal echocardiography of post-transcatheter tricuspid valve implant of a Melody valve within the Carpentier-Edwards valve (AVI 990 kb)

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Copyright information

© Springer Nature Switzerland AG 2019

Authors and Affiliations

  1. 1.Department of Pediatric CardiologyChildren’s Hospital Colorado, University of Colorado School of MedicineAuroraUSA
  2. 2.Taussig Heart Center, The Johns Hopkins Hospital and School of MedicineBaltimoreUSA

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