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Orbital Vascular Anomalies

  • Yvette Marie Santiago
  • Aaron Fay
Chapter

Abstract

Vascular anomalies comprise vascular neoplasms that result from active cell proliferation and vascular malformations which are congenital defects in vascular development. The distinction between tumors and malformations was recognized by the International Society for the Study of Vascular Anomalies (ISSVA) to provide a more clinically useful classification scheme and internationally consistent nomenclature. It focuses on a systematic approach to vascular lesions that correlates predictably with clinical history, disease course, and treatment options. Vascular tumors are further classified as benign, locally aggressive (borderline), or malignant. The most common of these is infantile hemangioma. Vascular malformations, on the other hand, are named after the vessel type(s) that compose them, i.e., venous malformation, lymphatic malformation, arteriovenous malformation, and assorted variations. Fistulae represent related vascular pathologies. Orbital vascular anomalies present unique challenges owing to the compartment they occupy and the critical structures therein. These lesions can be classified independent of tissue type, based on flow radiographic and clinical flow characteristics.

Keywords

Orbital vascular anomalies Orbital vascular tumors Hemangioma Orbital vascular malformations Lymphatic malformations Venous malformations AV fistula AV malformation Hemangiopericytoma 

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Copyright information

© Springer Nature Switzerland AG 2019

Authors and Affiliations

  • Yvette Marie Santiago
    • 1
  • Aaron Fay
    • 2
  1. 1.Eye InstituteSt. Luke’s Medical CenterQuezon CityPhilippines
  2. 2.Harvard Medical School, Department of OphthalmologyBostonUSA

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