Critical Care of Children with Heart Disease pp 507-519 | Cite as
Acute Myocarditis and Cardiomyopathies
Abstract
The definition and classification of cardiomyopathies was recently revised by an expert panel of the American Heart Association [1] following the initial classification by the World Health Organization in 1995 [2]. Cardiomyopathies are considered “a heterogeneous group of diseases of the myocardium associated with mechanical and/or electrical dysfunction that usually (but not invariably) exhibit inappropriate ventricular hypertrophy or dilatation and are due to a variety of causes that frequently are genetic” [1]. Cardiomyopathies are generally considered as primary (disease solely or predominantly confined to heart muscle) or secondary, showing pathological myocardial involvement secondary to a systemic or multiorgan disease process. Both forms are commonly seen in children, although primary forms predominate.
Keywords
Acute Heart Failure Hypoplastic Left Heart Syndrome Constrictive Pericarditis Ventricular Assist Device Noonan SyndromeReferences
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