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Subpulmonary Right Ventricle in Congenital Heart Disease

  • Christian Apitz
  • Heiner Latus
  • Dietmar SchranzEmail author
Chapter
Part of the Respiratory Medicine book series (RM)

Abstract

In this chapter we describe the role of the right ventricle in congenital heart disease associated with a volume and pressure overloaded right ventricle. Addressed is the interaction of the right ventricular with the pulmonary circulation and its electro-mechanical and left-to-right as well as right-to-left heart interactions. We highlight the importance of blood flow for cardiac growth, and the need for pathophysiology based therapeutic strategies. In addition, the differences between pulmonary hypertension in adults and children are emphasized.

Keywords

Pulmonary Arterial Hypertension Right Ventricle Pulmonary Valve Pulmonary Regurgitation Pulmonary Valve Replacement 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

Supplementary material

310219_1_En_5_MOESM1_ESM.avi (1.8 mb)
Video 5.1 Shown is a critical pulmonary stenosis in a newborn; the almost atretic pulmonary valve with intact ventricular septum was associated with a bipartite right ventricular morphology; the patient was postnatally referred with supra-systemic right ventricular pressure despite severely compromised function and associated tricuspid regurgitation. (AVI 1865 kb)
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Video 5.2a Shown is the echocardiography of the same patient as on Video 5.1. (AVI 9992 kb)
310219_1_En_5_MOESM2b_ESM.avi (7.2 mb)
Video 5.2b The recovered function of the unloaded right ventricle is demonstrated immediately after valve dilatation and duct stenting. (AVI 7409 kb)
310219_1_En_5_MOESM3_ESM.avi (4.9 mb)
Video 5.3 Shown is an angiography in anterior-posterior plane of an almost monopartite right ventricle in a newborn with pulmonary atresia and intact ventricular septum (PAT + IVS). The coronary perfusion is retrograde from the right ventricle (RV) with supra-systemic pressure to the ascending aorta (RV-dependent coronary circulation). (AVI 5013 kb)
310219_1_En_5_MOESM4_ESM.avi (1.1 mb)
Video 5.4 Shown is an MRI-movie in 4-chamber view; the right to left ventricular relationship based on a long-term untreated significant atrium septum defect should be demonstrated. Remarkable is the pseudo-hypoplasia of the unloaded left ventricle, which can be associated with a restrictive physiology. (AVI 1087 kb)
Video 5.5

Shown is an echocardiographic four-chamber view in a patient with Ebstein’s anomaly. By application of the strain-method the abnormal interventricular interaction can be nicely demonstrated. (AVI 23598 kb)

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Copyright information

© Springer Science+Business Media New York 2015

Authors and Affiliations

  • Christian Apitz
    • 1
  • Heiner Latus
    • 1
  • Dietmar Schranz
    • 1
    Email author
  1. 1.Department of Pediatric CardiologyJustus-Liebig-UniversityGiessenGermany

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