Symbrachydactyly

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Abstract

Symbrachydactyly is a distal manifestation of a transverse deficiency within group I failure of axis formation and/or differentiation and within the proximal distal outgrowth division. In its mildest form, the fingers are shortened due to absence of the middle phalanges and involved in varying degrees of syndactyly. Children with more severe forms of symbrachydactyly usually have either a thumb and a small finger separated by “nubbins”; or only have a thumb but are missing all four fingers, which are represented just by “nubbins”; or have absence of all five digits, which are represented just by “nubbins.” Surgical options for reconstruction of children with transverse failure or symbrachydactyly include nonvascularized toe phalangeal bone grafting, distraction osteogenesis, and microsurgical toe-to-hand transfers.

Keywords

Donor Site Morbidity Distraction Osteogenesis Extensor Tendon Proximal Phalanx Ulnar Collateral Ligament 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.
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Copyright information

© Springer Science+Business Media New York 2015

Authors and Affiliations

  1. 1.Department of Orthopaedic SurgeryUniversity of California, IrvineOrangeUSA
  2. 2.Department of Orthopedic SurgeryUniversity of California Irvine Medical Center and Shriners Hospital Los AngelesOrangeUSA

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