Classification and Epidemiology of Cerebellar Degenerations

  • Andreas Plaitakis
Chapter
Part of the Foundations of Neurology book series (FONY, volume 2)

Abstract

The cerebellar degenerations encompass a large number of heterogenous neurological disorders that are characterized pathologically by degeneration and atrophy of the cerebellum and its connections and clinically by disturbances of motor coordination or ataxia. Because involvement of the spinal cord may also occur in these cerebellar disorders, the term spinocerebellar degeneration has often been used interchangeable with the above broader term cerebellar degeneration. In other types, cerebellar atrophy can be found in combination with atrophic lesions of the basal ganglia, brain stem, spinal cord, and/or cerebral cortex. Such disorders may be best categorized under multiple system atrophy, although some authors will use this term only when they refer to disorders with coexisting progressive autonomic failure.

Keywords

Multiple System Atrophy Cerebellar Ataxia Spinocerebellar Ataxia Retinal Degeneration Cerebellar Degeneration 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.
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  • Andreas Plaitakis

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