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Supravalvular Aortic Stenosis

  • Anita SadeghpourEmail author
  • Azin Alizadehasl
Chapter

Abstract

Supravalvular aortic stenosis (sup AS) is the least common type of congenital left ventricular outflow tract (LVOT) obstruction. In the most common type of sup AS, there is a fixed aortic narrowing originating from just above the sinus of Valsalva which extends along a variable length of the aorta (hourglass type); the membranous type is the result of a fibrous or fibromuscular semicircular diaphragm with a small central opening in the lumen of the aorta, and diffuse hypoplasia of the ascending aorta illustrates the third type [1].

Keywords

Supravalvular aortic stenosis Williams syndrome Hourglass type Echocardiography Hypercalcemia 

Supplementary material

Video 37.1

Color flow Doppler study is helpful for identifying the level of the stenosis. In the supra aortic stenois turbulent flow originate above the AV (MPG 2576 kb)

Video 37.2

Transthoracic 2D and color Doppler study in apical 5 chamber view showing a discrete membrane above the Aortic valve (AV) that turbulent flow begins above the AV (MPG 2674 kb)

Video 37.3

Transthoracic 2D and color Doppler study in apical 5 chamber view showing a discrete membrane above the Aortic valve (AV) that turbulent flow begins above the AV (MPG 2674 kb)

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Copyright information

© Springer-Verlag London 2014

Authors and Affiliations

  1. 1.Echocardiography Lab, Department of CardiologyAdult Congenital Heart Disease Clinic, Rajaie Cardiovascular Medical and Research Center, Iran University of Medical ScienceTehranIran
  2. 2.Echocardiography Lab, Department of CardiologyRajaie Cardiovascular Medical and Research Center, Iran University of Medical ScienceTehranIran

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