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Congenital Aortic Valve Stenosis

  • Azin AlizadehaslEmail author
  • Anita Sadeghpour
Chapter

Abstract

Congenital aortic valve stenosis (AS) is a relatively common anomaly. Congenital AS occurs much more commonly in men, with a male to female ratio of 4:1. Related cardiac anomalies have been seen in up to 1/5 of patients. Patent ductus arteriosus (PDA) and coarctation of the aorta happen most often with AS [1].

Keywords

Aortic valve stenosis Echocardiography Bicuspid aortic valve Unicuspid aortic valve Aortic insufficiency (AI) 

Supplementary material

310404_1_En_35_MOESM1_ESM.avi (3.5 mb)
Video 35.1 Oval shape opening of the Bicuspid Aortic valve (BAV) in parasternal short-axis view, note the evaluation was done in systole (AVI 3618 kb)
Video 35.2

Transesophageal echocardiography showing thickened and calcified BAV in short axis view (WMV 628 kb)

Video 35.3

The catheter course is arterial; injection was performed in aortic root and showed doming of AV cusps due to bicuspid aortic valve (WMV 422 kb)

Video 35.4

Quadricuspid aortic valve in short axis and long axis transesophageal echocardiography associated with significant aortic regurgitation (WMV 544 kb)

Video 35.5

Quadricuspid aortic valve in short axis and long axis transesophageal echocardiography associated with significant aortic regurgitation (WMV 333 kb)

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Copyright information

© Springer-Verlag London 2014

Authors and Affiliations

  1. 1.Echocardiography Lab, Department of CardiologyRajaie Cardiovascular Medical and Research Center, Iran University of Medical ScienceTehranIran
  2. 2.Echocardiography Lab, Department of CardiologyAdult Congenital Heart Disease Clinic, Rajaie Cardiovascular Medical and Research Center, Iran University of Medical ScienceTehranIran

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