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Complete Transposition of the Great Arteries (d-TGA) and the Senning and Mustard Procedures

  • Anita SadeghpourEmail author
  • Azin Alizadehasl
  • Mohammad Esmaeil Rezaei
Chapter

Abstract

This common cyanotic congenital heart defect (5–10 % of all CHD cases) is a cono-truncal abnormality characterized by ventriculo-arterial discordance in the presence of atrioventricular concordance. In most patients, the apex of the heart points to the left (levocardia). The aorta is usually located anterior and rightward to the pulmonary artery, but any relationship between great arteries is possible.

Keywords

Complete transposition of the great arteries (d-TGA) The Senning procedure Mustard procedures Transesophageal echocardiography Arterial switch 

Supplementary material

Video 33.1

Parasternal long axis view showing anterior located right ventricle (RV) associated with transposed great arteries and anterior located aorta (AO) (MPG 1388 kb)

Video 33.2

Parasternal long axis view showing anterior located right ventricle (RV) associated with transposed great arteries and anterior located aorta (AO) (MPG 1896 kb)

Video 33.3

Parasternal short axis view demonstrating dilated aorta(AO), hypoplastic pulmonary artery and anterior located AO associated with ASD (MPG 1224 kb)

Video 33.4

Apical 4 chamber view showing D-Loop ventricle associated with a large VSD (MPG 1556 kb)

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Video 33.5 CMR reliably demonstrates the ventricular and arterial looping besides the ventricular size and function (AVI 3887 kb)
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Video 33.6 Transthoracic echocardiography in 4 chamber view showing pulmonary venous chamber drains to the morphologic RV and systemic venous chamber o the left ventricle with no obstruction in 2D study (WMV 1006 kb)
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Video 33.7 Transthoracic echocardiography in 4 chamber view showing pulmonary venous chamber drains to the morphologic RV and systemic venous chamber o the left ventricle with no obstruction in 2D study (WMV 738 kb)
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Video 33.8 Patent systemic venous chamber with no leakage as demonstrated in right hand contrast injection (WMV 308 kb)
Video 33.9

Patent systemic venous chamber with no obstruction in SVC anastomosis. SVC anastomosis is patent if contrast injected into a peripheral arm vein promptly enters the SVA, In obstruction at the SVC, azygous or other collaterals to IVC will cause contrast to first enter the IVC and then to SVA (WMV 1425 kb)

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Copyright information

© Springer-Verlag London 2014

Authors and Affiliations

  • Anita Sadeghpour
    • 1
    Email author
  • Azin Alizadehasl
    • 2
  • Mohammad Esmaeil Rezaei
    • 3
  1. 1.Echocardiography Lab, Department of CardiologyAdult Congenital Heart Disease Clinic, Rajaie Cardiovascular Medical and Research Center, Iran University of Medical ScienceTehranIran
  2. 2.Echocardiography Lab, Department of CardiologyRajaie Cardiovascular Medical and Research Center, Iran University of Medical ScienceTehranIran
  3. 3.Department of CardiologyRajaie Cardiovascular Medical and Research CenterTehranIran

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