Atrioventricular Septal Defect (AVSD)

  • Azin AlizadehaslEmail author
  • Anita Sadeghpour
  • Nehzat Akiash


Atrioventricular septal defect (AVSD) consists of a group of anomalies with the common main pathology of the absence of the atrioventricular (AV) septum associated with the abnormalities of the AV valves [1]. AVSD has been divided into the two main categories as the partial and complete forms and two other subtypes as the transitional (which is the subtype of partial AVSD) and intermediate (which is the subtype of complete AVSD). In complete AVSD, a primum ASD is concomitant with an inlet-type ventricular septal defect (VSD), and a common AV valve has only single annulus. In addition, transitional AVSD is used when a partial AVSD also has a small inlet-type VSD that is partially obstructed via chordal attachments to the intraventricular septum. Also, intermediate subtype of AVSD has separate right and left AV valve orifices even though having only one common annulus. These distinct orifices are referred to as right and left AV valve orifices rather than mitral and tricuspid [2, 3].


Atrioventricular Septal Defect (AVSD) Complete AVSD Partial AVSD Transitional AVSD Primum ASD 

Supplementary material

Video 23.1

Complete AVSD with a common AV valve, large ostium primum type atrial septal defect’ and large inlet type inter-ventricular septum defect (WMV 281 kb)

Video 23.2

Complete AVSD with common AV valve and it’s five leaflets (superior bridging, left mural, inferior bridging, right mural and right antero-superior leaflets) (WMV 394 kb)

310404_1_En_23_MOESM3_ESM.mpg (790 kb)
Video 23.3 Complete AVSD, Rastelli Type A, the superior bridging leaflet is attached to the crest of ventricular septum (MPG 790 kb)
Video 23.4

Complete AVSD, Rastelli Type C in short axis and 4 chamber views, the superior bridging leaflet is attached to the papillary muscle on RV free wall (WMV 294 kb)


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Copyright information

© Springer-Verlag London 2014

Authors and Affiliations

  • Azin Alizadehasl
    • 1
    Email author
  • Anita Sadeghpour
    • 2
  • Nehzat Akiash
    • 3
  1. 1.Echocardiography Lab, Department of CardiologyRajaie Cardiovascular Medical and Research Center, Iran University of Medical ScienceTehranIran
  2. 2.Echocardiography Lab, Department of CardiologyAdult Congenital Heart Disease Clinic, Rajaie Cardiovascular Medical and Research Center, Iran University of Medical ScienceTehranIran
  3. 3.Department of CardiologyRajaie Cardiovascular Medical and Research CenterTehranIran

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