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Thoracic Aortic Surgery in Marfan Syndrome

  • Pouya Youssefi
  • Marjan JahangiriEmail author
Chapter

Abstract

One of the cardinal features of Marfan Syndrome (MFS) is involvement of the cardiovascular system, with predominant effect on the thoracic aorta. The most life-threatening complication of MFS is aneurysm of the thoracic aorta. This can lead to acute aortic dissection or rupture. The mainstay of surgical treatment of the thoracic aorta in Marfan patients is to prophylactically replace or repair part of the thoracic aorta before dissection or rupture occurs. However, it also encompasses emergency surgical management of acute aortic dissection when this lethal disorder does present itself.

Keywords

Activated clotting time (ACT) measurements Age Alcohol intake Anaesthetic Anatomy Angiotensin II blockers Annulus Antegrade infusion Anticoagulation Aortic arch Aortic dissection Aortic valve leaflets Aortic valve replacement Aortic valve sparing root Apico-aortic shunt Arterial cannulation Ascending aorta Axillary artery Bentall procedure Bioprosthetic valve Bleeding Blood pressure Brachiocephalic artery Caesarean section Cannulae Cardiopulmonary bypass Cautery Cerebral perfusion Cerebrospinal fluid (CSF) pressure Children Circle of Willis Clamshell thoracotomy Classification Co-aptation Collateralisation Commissures Common carotid artery Composite valve-graft replacement Coronary arteries Coronary buttons Covered stent Cross-clamp Cross-sectional area of the root Dacron grafts Dacron tube graft David V – Standford Modification technique Debakey classification Dental assessment Descending aorta Descending thoracic aorta Descending thoracic/thoracoabdominal aorta Diaphragm Dr Tirone David Dural ectasia Elderly Elephant trunk technique Emergency surgery Endocarditis European Society of Cardiology guidelines False lumen Foetal blood flow monitoring Foetal malformations Foetal medicine Foetal monitoring Foetus Growth Heparinised High arched palate Homografts Hormonal changes Hypothermic circulatory arrest Infantile Intercostal arteries Intima Ischaemia Island anastomosis Joint laxity Landing zone Leaflet hinge-lines Life expectancy Lifestyle choice Limb ischaemia Liver disease Maternal mortality Mattress sutures Median sternotomy Mesenteric ischaemia Meta-analysis Mini-J sternotomy Morbidity Mortality Myocardial infarction Myocardial protection Neo-sinuses Open heart surgery Paediatrics Paraplegia Pericardium Peripartum period Positioning Preconception assessment Pregnancy Pregnant Pre-operative assessment Preterm delivery Professor Sir Magdi Yacoub Prognathism Prosthetic aortic valve Pulmonary autotransplantation Pulmonary vasculature Recurrent laryngeal nerve Redo operations Reduced neck extension Reimplantation Reimplantation technique Reimplanted Re-intervention Re-intervention rate Remodelling Renal failure Rewarming Risk Ross procedure Scoliosis Selective antegrade Sino-tubular junction Sinuses of Valsalva Spinal cord Spinal cord perfusion Spontaneous pneumothorax Stanford classification Starr-Edwards valve Stent-grafting Steroids Stroke Subclavian artery Superior vena cava Survival rates Suture line Tamponade Teenage Temporo-mandibular joint Third trimester Thoracoabdominal aneurysms Thoraco-abdominal aortic replacement Thoracotomy Thrombo-embolic event rates Thromboembolism Tracheal intubation Trans-catheter valve-in-valve implantation True lumen Tube graft Vagus nerve Valve dysfunction Valve-sparing root replacement (VSRR) Vertebral artery Warfarin Whole body perfusion Yacoub 

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Copyright information

© Springer-Verlag London 2016

Authors and Affiliations

  1. 1.Department of Cardiothoracic SurgerySt. George’s HospitalLondonUK

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