Aortic Anomalies

  • Sylvia S. M. ChenEmail author
  • Raad H. Mohiaddin


Aortic congenital anomalies are common and comprised of a heterogenous group of conditions that may be due to either embryological or vessel wall architectural defects. Imaging is crucial for diagnosis, management, follow-up and reassessment after intervention of these conditions. Cardiovascular magnetic resonance (CMR) is a valuable non-invasive imaging method for providing detailed anatomical, functional and haemodynamic information on a wide spectrum of aortic anomalies and intra- and extracardiac associated abnormalities. The technique is radiation free and is ideally suited for diagnoses as well as serial follow-up pre and post interventions such as a dilated aortic root in Marfan syndrome and aortic coarctation. This chapter reviews the role of CMR in the management of a wide spectrum of congenital aortic anomalies and provides CMR scanning protocols and clinical reporting of the anomalies both in the native and post-repair states.


Cardiovascular Magnetic Resonance Magnetic Resonance Angiography Aortic Root Patent Ductus Arteriosus Ventricular Septal Defect 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

Supplementary material

Movie 12.1

Multi-intensity projection (MIP) reconstruction of MRA after contrast enhancement in severe native coarctation of the aorta with collaterals (AVI 10795 KB)

Movie 12.2

Aneurysm at the site of previous coarctation repair. There is persistent flow into the aneurysm despite previous stent implantation (AVI 11544 KB)

Movie 12.3

Surface rendered 3D reconstruction after contrast enhanced MRA of truncus arteriosus type 1 with a short main pulmonary after arising from the common arterial trunk (AVI 15676 KB)

Movie 12.4

Surface rendered 3D reconstruction after contrast enhanced MRA showing a diverticulum of Kommerell at the origin of an anomalous left subclavian artery from a right aortic arch (AVI 11662 KB)

Movie 12.5

Surface rendered 3D reconstruction after contrast enhanced MRA of a double aortic arch (AVI 11528 KB)


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Copyright information

© Springer-Verlag London 2012

Authors and Affiliations

  1. 1.Cardiovascular Magnetic Resonance UnitThe Royal Brompton HospitalLondonUK
  2. 2.Cardiovascular Magnetic Resonance UnitRoyal Brompton Hospital and National Heart and Lung Institute, Imperial College LondonLondonUK

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