Lymphedema pp 11-28 | Cite as

Etiology and Classification of Lymphatic Disorders

  • Stanley G. Rockson


Beyond lymphedema, in its diverse manifestations, there is a spectrum of human disease that directly or indirectly alters lymphatic structure and function. Not surprisingly, the symptomatic and objective presentation of these patients is quite heterogeneous. Diagnosis and differential diagnosis pose distinct challenges. In this overview, the various categories of lymphatic disease are enumerated and viewed through the prism of lymphatic embryological development (Chap. 4).


Noonan Syndrome Lymphatic Endothelial Cell Lymphatic Vasculature Secondary Lymphedema Lymphangioma Circumscriptum 
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Copyright information

© Springer-Verlag London Limited 2011

Authors and Affiliations

  • Stanley G. Rockson
    • 1
  1. 1.Division of Cardiovascular MedicineStanford University School of Medicine, Falk Cardiovascular Research CenterStanfordUSA

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