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Tumors and Related Lesions of the Retinal Pigmented Epithelium

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Ocular Oncology

Part of the book series: Retina Atlas ((RA))

Abstract

There are a variety of pigment epithelial tumors, including benign and malignant types. Some are considered congenital such as congenital hypertrophy of the retinal pigment epithelium (CHRPE) (solitary and multifocal), congenital simple hamartoma, and torpedo maculopathy. Some are presumed acquired such as adenoma and adenoma of the pigment epithelium. These lesions can clinically simulate malignant tumors, particularly malignant melanoma of the iris, ciliary body, and choroid (Shields and Shields 2015; Shields and Shields 2017a, b, c).

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Authors and Affiliations

  1. Ocular Oncology Service, Wills Eye Hospital, Philadelphia, PA, USA

    Carol L. Shields & Jerry A. Shields

  2. Department of Ophthalmology, Thomas Jefferson Unversity, Philadelphia, PA, USA

    Carol L. Shields & Jerry A. Shields

Authors
  1. Carol L. Shields
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  2. Jerry A. Shields
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Editors and Affiliations

  1. Department of Ophthalmology, Faculty of Medicine, Ramathibodi Hospital, Mahidol University, Bangkok, Thailand

    Duangnate Rojanaporn

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Shields, C.L., Shields, J.A. (2019). Tumors and Related Lesions of the Retinal Pigmented Epithelium. In: Rojanaporn, D. (eds) Ocular Oncology. Retina Atlas. Springer, Singapore. https://doi.org/10.1007/978-981-13-2336-2_11

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  • DOI: https://doi.org/10.1007/978-981-13-2336-2_11

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  • Print ISBN: 978-981-13-2335-5

  • Online ISBN: 978-981-13-2336-2

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