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Kapilläre Nävi und andere vaskuläre Malformationen

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Book cover Braun-Falco’s Dermatologie, Venerologie und Allergologie

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Zusammenfassung

Die Bezeichnung kapilläre Malformation hat auf internationaler Ebene Verwirrung gestiftet. Die hier vorgeschlagene Klassifikation befolgt das Prinzip, dass jeder spezifischen Hautkrankheit ein spezifischer Name zukommt. Kapilläre Nävi sind Naevus flammeus, Portweinnävus vom Proteus-Typ, Portweinnävus vom CLOVES-Typ, Naevus roseus, rhodoider Nävus, Cutis marmorata teleangiectatica congenita, Livedo reticularis congenita, segmentales Angioma serpiginosum, Naevus anaemicus, Naevus syringocapillaris, Naevus vascularis mixtus und Angiokeratoma circumscriptum. Weitere mögliche kapilläre Nävi sind mesotroper Portweinfleck, Carter-Mirzaa-Flecken sowie unilaterale nävoide Teleangiektasien vom punktförmigen oder fleckförmigen Typ. Hinzu kommen der segmentale Naevus venosus und die hereditären kleinen venösen Nävi. Lymphatische Malformationen umfassen Naevus lymphangioreticularis und die lymphatische Kokardenmalformation, die bislang als Hämangiom fehlgedeutet worden ist.

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Authors and Affiliations

  1. Klinik für Dermatologie und Venerologie, Universitätsklinikum Freiburg, Hauptstr. 7, 79104, Freiburg, Deutschland

    Rudolf Happle

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  1. Rudolf Happle
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Correspondence to Rudolf Happle .

Editor information

Editors and Affiliations

  1. Klinik und Poliklinik für Dermatologie und Allergologie, Universitätsklinikum München, München, Germany

    Gerd Plewig

  2. Klinik und Poliklinik für Dermatologie und Allergologie, Universitätsklinikum München, München, Germany

    Thomas Ruzicka

  3. Klinik für Dermatologie, Venerologie und Allergologie, J.W.Goethe-Universität, Frankfurt, Germany

    Roland Kaufmann

  4. Klinik für Dermatologie und Allergologie, Universitätsklinikum Marburg, Marburg, Germany

    Michael Hertl

Section Editor information

  1. Klinik für Dermatologie und Allergologie, Universitätsklinikum Marburg, Baldingerstr.1, 35043, Marburg, Deutschland

    Michael Hertl

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Happle, R. (2018). Kapilläre Nävi und andere vaskuläre Malformationen. In: Plewig, G., Ruzicka, T., Kaufmann, R., Hertl, M. (eds) Braun-Falco’s Dermatologie, Venerologie und Allergologie. Springer Reference Medizin. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-662-49544-5_66

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  • DOI: https://doi.org/10.1007/978-3-662-49544-5_66

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