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Sklerodermie

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Braun-Falco’s Dermatologie, Venerologie und Allergologie

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Zusammenfassung

Bei den Sklerodermien handelt es sich um eine heterogene Gruppe chronisch-entzündlicher fibrosierender Erkrankungen unbekannter Ätiologie. Die zirkumskripte Sklerodermie betrifft vornehmlich umschriebene Hautareale, kann aber abhängig vom Subtyp auch hautnahe Strukturen wie Fettgewebe, Muskeln, Gelenke und Knochen befallen. Bei der systemischen Sklerodermie/Sklerose wird die Fibrose der Haut von einer sehr unterschiedlich ausgeprägten Beteiligung innerer Organe (Gastrointestinaltrakt, Lunge, Herz, Niere) sowie der Muskulatur und Gelenke begleitet. Es handelt sich um zwei eigenständige Krankheitsbilder. Hiervon abzugrenzen ist das weite Spektrum der Sklerodermie-ähnlichen Erkrankungen oder Pseudosklerodermien.

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Authors and Affiliations

  1. Klinik und Poliklinik für Dermatologie und Venerologie, Universität zu Köln, Kerpener Str. 62, 50937, Köln, Deutschland

    Nicolas Hunzelmann & Thomas Krieg

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  1. Nicolas Hunzelmann
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  2. Thomas Krieg
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Correspondence to Nicolas Hunzelmann .

Editor information

Editors and Affiliations

  1. Klinik und Poliklinik für Dermatologie und Allergologie, Universitätsklinikum München, München, Germany

    Gerd Plewig

  2. Klinik und Poliklinik für Dermatologie und Allergologie, Universitätsklinikum München, München, Germany

    Thomas Ruzicka

  3. Klinik für Dermatologie, Venerologie und Allergologie, J.W.Goethe-Universität, Frankfurt, Germany

    Roland Kaufmann

  4. Klinik für Dermatologie und Allergologie, Universitätsklinikum Marburg, Marburg, Germany

    Michael Hertl

Section Editor information

  1. Zentrum für Hautkrankheiten, Deutschhausstraße 9, 35037, Marburg, Germany

    Michael Hertl

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Hunzelmann, N., Krieg, T. (2018). Sklerodermie. In: Plewig, G., Ruzicka, T., Kaufmann, R., Hertl, M. (eds) Braun-Falco’s Dermatologie, Venerologie und Allergologie. Springer Reference Medizin. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-662-49544-5_53

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  • DOI: https://doi.org/10.1007/978-3-662-49544-5_53

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