Skip to main content

Abstract

There are no accurate data on the prevalence and incidence of the clinically multifaceted group of parapsoriasis. The clinical variables in this group have a chronic course with only few clinical symptoms, if any; they may remain underreported although patients with parapsoriasis have an increased risk of subsequent cancers and increased mortality [1]. The group of parapsoriasis comprises several inhomogeneous, chronic-intermittently developing skin diseases which may clinically mimic psoriasis but are unrelated to each other with respect to their pathogenesis, histopathology, and response to treatment. Their etiology is unknown and the pathogenetic mechanisms are not fully understood. A part of these entities present inflammatory features as a reactive T-cell skin disease with vasculitis, often arising following infections, and another part is considered as precursor or early lymphoproliferative disorder with long-term progression into cutaneous T-cell lymphoma (CTCL). The majority of the entities included are associated with male predominance.

This is a preview of subscription content, log in via an institution to check access.

Access this chapter

Chapter
USD 29.95
Price excludes VAT (USA)
  • Available as PDF
  • Read on any device
  • Instant download
  • Own it forever
eBook
USD 149.00
Price excludes VAT (USA)
  • Available as EPUB and PDF
  • Read on any device
  • Instant download
  • Own it forever
Softcover Book
USD 199.99
Price excludes VAT (USA)
  • Compact, lightweight edition
  • Dispatched in 3 to 5 business days
  • Free shipping worldwide - see info
Hardcover Book
USD 279.99
Price excludes VAT (USA)
  • Durable hardcover edition
  • Dispatched in 3 to 5 business days
  • Free shipping worldwide - see info

Tax calculation will be finalised at checkout

Purchases are for personal use only

Institutional subscriptions

References

  1. Lindahl LM, Fenger-Grøn M, Iversen L. Subsequent cancers, mortality, and causes of death in patients with mycosis fungoides and parapsoriasis: a Danish nationwide, population-based cohort study. J Am Acad Dermatol. 2014;71:529–35.

    Article  PubMed  Google Scholar 

  2. Weinberg JM, Kristal L, Chooback L, et al. The clonal nature of pityriasis lichenoides. Arch Dermatol. 2002;138:1063–7.

    Article  PubMed  Google Scholar 

  3. Lane TN, Parker SS. Pityriasis lichenoides chronica in black patients. Cutis. 2010;85:125–9.

    PubMed  Google Scholar 

  4. Maranda EL, Smith M, Nguyen AH, et al. Phototherapy for pityriasis lichenoides in the pediatric population: a review of the published literature. Am J Clin Dermatol. 2016;17:583–91.

    Article  PubMed  Google Scholar 

  5. Fernández-Guarino M, Aboin-Gonzalez S, Ciudad Blanco C, et al. Treatment of adult diffuse pityriasis lichenoides chronica with narrowband ultraviolet B: experience and literature review. Clin Exp Dermatol. 2017;42:303–5.

    Article  PubMed  Google Scholar 

  6. Koh WL, Koh MJ, Tay YK. Pityriasis lichenoides in an Asian population. Int J Dermatol. 2013;52:1495–9.

    Article  PubMed  Google Scholar 

  7. Ankad BS, Beergouder SL. Pityriasis lichenoides et varioliformis acuta in skin of color: new observations by dermoscopy. Dermatol Pract Concept. 2017;7:27–34.

    Article  PubMed  PubMed Central  Google Scholar 

  8. English JC, Collins M, Bryant-Bruce C. Pityriasis lichenoides varioliformis acuta and group-a beta hemolytic streptococcal infection. Int J Dermatol. 1995;34:642–4.

    Article  PubMed  Google Scholar 

  9. Edwards BL, Bonagura VR, Valacer DJ, et al. Mucha Habermann’s disease and arthritis: possible association with reactivated Epstein-Barr virus infection. J Rheumatol. 1989;16:387–9.

    PubMed  CAS  Google Scholar 

  10. Nanda A, Alshalfan F, Al-Otaibi M, et al. Febrile ulceronecrotic Mucha-Habermann disease (pityriasis lichenoides et varioliformis acuta fulminans) associated with parvovirus infection. Am J Dermatopathol. 2013;35:503–6.

    Article  PubMed  Google Scholar 

  11. Fölster-Holst R, Zawar VP, Chuh A. Paraviral exanthems. Expert Rev Anti-Infect Ther. 2016;14:601–11.

    Article  CAS  PubMed  Google Scholar 

  12. Khachemoune A, Blyumin ML. Pityriasis lichenoides: pathophysiology, classification, and treatment. Am J Clin Dermatol. 2007;8:29–36.

    Article  PubMed  Google Scholar 

  13. Romaní J, Puig L, Fernández-Figueras MT, et al. Pityriasis lichenoides in children: clinicopathologic review of 22 patients. Pediatr Dermatol. 1998;15:1–6.

    Article  PubMed  Google Scholar 

  14. Yang CC, Lee JY, Chen W. Febrile ulceronecrotic Mucha-Habermann disease with extensive skin necrosis in intertriginous areas. Eur J Dermatol. 2003;13:493–6.

    PubMed  Google Scholar 

  15. Sotiriou E, Patsatsi A, Tsorova C, et al. Febrile ulceronecrotic Mucha-Habermann disease: a case report and review of the literature. Acta Derm Venereol. 2008;88:350–5.

    PubMed  Google Scholar 

  16. Suárez J, López B, Villalba R, et al. Febrile ulceronecrotic Mucha-Habermann disease: a case report and review of the literature. Dermatology. 1996;192:277–9.

    Article  PubMed  Google Scholar 

  17. Griffith-Bauer K, Leitenberger SL, Krol A. Febrile ulceronecrotic Mucha-Habermann disease: two cases with excellent response to methotrexate. Pediatr Dermatol. 2015;32:e307–8.

    Article  PubMed  Google Scholar 

  18. Meziane L, Caudron A, Dhaille F, et al. Febrile ulceronecrotic Mucha-Habermann disease: treatment with infliximab and intravenous immunoglobulins and review of the literature. Dermatology. 2012;225:344–8.

    Article  CAS  PubMed  Google Scholar 

  19. Kreuter A, Knispel S, Wieland U, et al. Complete resolution of febrile ulceronecrotic Mucha-Habermann disease following infliximab therapy. J Dtsch Dermatol Ges. 2016;14:184–6.

    PubMed  Google Scholar 

  20. Kikuchi A, Naka W, Harada T, et al. Parapsoriasis en plaques: its potential for progression to malignant lymphoma. J Am Acad Dermatol. 1993;29:419–22.

    Article  CAS  PubMed  Google Scholar 

  21. Väkevä L, Sarna S, Vaalasti A, et al. A retrospective study of the probability of the evolution of parapsoriasis en plaques into mycosis fungoides. Acta Derm Venereol. 2005;85:318–23.

    Article  PubMed  Google Scholar 

  22. Bloom B, Marchbein S, Fischer M, et al. Poikilodermatous mycosis fungoides. Dermatol Online J. 2012;18(12):4.

    Google Scholar 

  23. Shiomi T, Monobe Y, Kuwabara C, et al. Poikilodermatous mycosis fungoides with a CD8+ CD56+ immunophenotype: a case report and literature review. J Cutan Pathol. 2013;40:317–20.

    Article  PubMed  Google Scholar 

  24. Wain EM, Orchard GE, Mayou S, et al. Mycosis fungoides with a CD56+ immunophenotype. J Am Acad Dermatol. 2005;53:158–63.

    Article  PubMed  Google Scholar 

Download references

Author information

Authors and Affiliations

Authors

Corresponding author

Correspondence to Constantin E. Orfanos M.D. .

Editor information

Editors and Affiliations

Rights and permissions

Reprints and permissions

Copyright information

© 2018 Springer International Publishing AG, part of Springer Nature

About this chapter

Check for updates. Verify currency and authenticity via CrossMark

Cite this chapter

Orfanos, C.E. (2018). Parapsoriasis. In: Orfanos, C., Zouboulis, C., Assaf, C. (eds) Pigmented Ethnic Skin and Imported Dermatoses. Springer, Cham. https://doi.org/10.1007/978-3-319-69422-1_22

Download citation

  • DOI: https://doi.org/10.1007/978-3-319-69422-1_22

  • Published:

  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-319-69421-4

  • Online ISBN: 978-3-319-69422-1

  • eBook Packages: MedicineMedicine (R0)

Publish with us

Policies and ethics