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Adult Congenital Heart Disease in Clinical Practice pp 151–163Cite as

Anomalous Pulmonary Venous Return

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Part of the book series: In Clinical Practice ((ICP))

Abstract

The incidence of partial anomalous pulmonary venous return is estimated to be at least 7 per 1000 individuals. The number and size of the anomalous vessels will define the size of the left-to-right shunt, and the severity of presentation can vary from mild disease identified incidentanlly to right-sided volume overload, severe pulmonary hypertension, and right ventricular failure. This chapter covers the anatomy and physiology of the disease, options and indications for surgical repair, and the management of adult survivors. Total anomalous pulmonary venous return is a rare but severe manifestation of anomalous pulmonary venous return generally presenting in infancy, but also receives mention in this chapter.

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Author information

Authors and Affiliations

  1. Massachusetts General Hospital, Boston, MA, USA

    Jonathan Kochav M.D.

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  1. Jonathan Kochav M.D.
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Editors and Affiliations

  1. Massachusetts General Hospital Heart Center, Boston, MA, USA

    Doreen DeFaria Yeh

  2. Massachusetts General Hospital Heart Center, Boston, MA, USA

    Ami Bhatt

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Kochav, J. (2018). Anomalous Pulmonary Venous Return. In: DeFaria Yeh, D., Bhatt, A. (eds) Adult Congenital Heart Disease in Clinical Practice. In Clinical Practice. Springer, Cham. https://doi.org/10.1007/978-3-319-67420-9_11

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  • DOI: https://doi.org/10.1007/978-3-319-67420-9_11

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-319-67418-6

  • Online ISBN: 978-3-319-67420-9

  • eBook Packages: MedicineMedicine (R0)

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