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Von Hippel–Lindau Syndrome

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Consults in Obstetric Anesthesiology

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Abstract

Von Hippel–Lindau syndrome (VHL) is a heritable neoplastic disease resulting in multisystem carcinoma, benign tumors, and cysts. VHL is inherited in an autosomal dominant manner and could result in benign or malignant tumors, with high penetrance affecting multiple organ systems, including the central nervous system (CNS) and visceral organs [1]. Incidences of VHL are associated with a germline mutation of a tumor suppressor gene, VHL, on the short arm of chromosome 3 (3p25.5) [2].

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Authors and Affiliations

  1. Department of Anesthesiology, Brigham and Women’s Hospital, Harvard Medical School, Boston, MA, USA

    Jie Zhou M.D., M.S., M.B.A. & Xiaoran Li M.D., M.S.

Authors
  1. Jie Zhou M.D., M.S., M.B.A.
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  2. Xiaoran Li M.D., M.S.
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Correspondence to Jie Zhou M.D., M.S., M.B.A. .

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Editors and Affiliations

  1. Associate Professor, Department of Anesthesiology, Columbia University Medical Center, New York, NY, USA

    Suzanne K. W. Mankowitz

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Zhou, J., Li, X. (2018). Von Hippel–Lindau Syndrome. In: Mankowitz, S. (eds) Consults in Obstetric Anesthesiology. Springer, Cham. https://doi.org/10.1007/978-3-319-59680-8_178

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  • DOI: https://doi.org/10.1007/978-3-319-59680-8_178

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-319-59679-2

  • Online ISBN: 978-3-319-59680-8

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