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Diagnosis and Management of Marfan Syndrome pp 101–125Cite as

Thoracic Aortic Surgery in Marfan Syndrome

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Abstract

One of the cardinal features of Marfan Syndrome (MFS) is involvement of the cardiovascular system, with predominant effect on the thoracic aorta. The most life-threatening complication of MFS is aneurysm of the thoracic aorta. This can lead to acute aortic dissection or rupture. The mainstay of surgical treatment of the thoracic aorta in Marfan patients is to prophylactically replace or repair part of the thoracic aorta before dissection or rupture occurs. However, it also encompasses emergency surgical management of acute aortic dissection when this lethal disorder does present itself.

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Authors and Affiliations

  1. Department of Cardiothoracic Surgery, St. George’s Hospital, London, UK

    Pouya Youssefi BSc (Hons) MBBS MRCS(Eng) & Marjan Jahangiri FRCS(CTh)

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  1. Pouya Youssefi BSc (Hons) MBBS MRCS(Eng)
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  2. Marjan Jahangiri FRCS(CTh)
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Correspondence to Marjan Jahangiri FRCS(CTh) .

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Editors and Affiliations

  1. Cardiovascular & Cell Sciences Research, St George's, University of London, London, United Kingdom

    Anne H. Child

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© 2016 Springer-Verlag London

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Youssefi, P., Jahangiri, M. (2016). Thoracic Aortic Surgery in Marfan Syndrome. In: Child, A. (eds) Diagnosis and Management of Marfan Syndrome. Springer, London. https://doi.org/10.1007/978-1-4471-5442-6_9

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  • DOI: https://doi.org/10.1007/978-1-4471-5442-6_9

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  • Publisher Name: Springer, London

  • Print ISBN: 978-1-4471-5441-9

  • Online ISBN: 978-1-4471-5442-6

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