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Anomalies of the Systemic and Pulmonary Arteries

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Congenital Heart Diseases in Adults

Part of the book series: Medical Radiology ((Med Radiol Diagn Imaging))

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Abstract

Congenital abnormalities of the thoracic systemic and pulmonary arteries can occur in isolation or in the setting of a complex cardiovascular malformation. Severe or complex vascular defects are usually diagnosed and corrected in childhood. Infrequently, anomalies of the systemic and pulmonary arteries present during adulthood. After correction of a cardiovascular malformation most children survive into adulthood. In adults, the most common indication for imaging is to evaluate post-treatment sequelae. Understanding the underlying pathology and possible complications that may occur during follow-up is essential for planning imaging studies. Furthermore, knowledge on the different imaging modalities, including their strengths and limitations for assessing anomalies of the systemic and pulmonary arteries, is important.

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Author information

Authors and Affiliations

  1. Department of Paediatrics, Willem Alexander Children’s Hospital, Leiden University Medical Center, Leiden, The Netherlands

    Arno A. W. Roest M.D., Ph.D.

  2. Section Head of Cardiothoracic Radiology, Department of Radiology, Leiden University Medical Center, Leiden, The Netherlands

    Lucia J. M. Kroft M.D., Ph.D.

  3. Section Head, Cardiovascular Magnetic Resonance, The Hospital for Sick Children, University of Toronto, Toronto, ON, Canada

    Lars Grosse-Wortmann M.D., F.R.C.P.S.C.

Authors
  1. Arno A. W. Roest M.D., Ph.D.
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  2. Lucia J. M. Kroft M.D., Ph.D.
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  3. Lars Grosse-Wortmann M.D., F.R.C.P.S.C.
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Correspondence to Arno A. W. Roest M.D., Ph.D. .

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Editors and Affiliations

  1. Diagnostic and Interventional Radiology, Chirurgisches Klinikum München Süd, Munich, Germany; Radiology, Internistisches Klinikum München Süd, Munich, Germany

    Sebastian Ley

  2. Department of Radiology, Pediatric Radiology, Ludwig-Maximilians-University of Munich, Munich, Germany

    Julia Ley-Zaporozhan

1 Electronic Supplementary Material

14-Year old male patient with recurrent pulmonary infection. CT angiography showing complete vascular ring: double aortic arch with large right arch and small left arch with an atretic segment (fibrous strand) in connection to the descending aorta. The movie highlights the symmetrical branching of the arch vessels and the small left arch with an atretic segment. See Fig. 11 for the vessel anatomy (AVI 123654 kb)

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Roest, A.A.W., Kroft, L.J.M., Grosse-Wortmann, L. (2018). Anomalies of the Systemic and Pulmonary Arteries. In: Ley, S., Ley-Zaporozhan, J. (eds) Congenital Heart Diseases in Adults. Medical Radiology(). Springer, Cham. https://doi.org/10.1007/174_2017_165

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  • DOI: https://doi.org/10.1007/174_2017_165

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