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Auto-Inflammatory Syndromes

Pathophysiology, Diagnosis, and Management

  • Book
  • © 2019


  • Provides thorough, up-to-date information and clinical applications for auto-inflammatory syndromes
  • Includes basic science and pathophysiology of these diseases to inform clinical decision making
  • Covers rare and rarely documented diseases in adults and pediatric patients, including systemic idiopathic arthritis, still’s disease, papa syndrome, and sweets syndrome

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About this book

This book provides an overview of auto-inflammatory syndromes, covering the underlying immune mechanisms that lead to their development, specific disease presentations, and clinical treatment guidelines. The book is divided into two sections, adult and pediatric, with chapters focusing on individuals diseases such as systemic arthritis, hyper-IgD, pap syndrome, idiopathic recurrent pericarditis, and familial Mediterranean fever. Chapters incorporate the most recent advances in disease pathophysiology and examine the underlying inductive and effector mechanisms and therapies that relate to each auto-inflammatory disorder at the genetic, molecular, cellular, and epidemiologic levels. The book also discusses the research behind auto-inflammatory disorders to offer detailed clinical guidelines regarding diagnostic techniques, treatment plans, and advice on how to best transition pediatric patients into adult treatment. This is an invaluable reference on auto-inflammatory syndromes for clinicians and researchers in pediatric and adult rheumatology and immunology.

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Table of contents (22 chapters)

  1. Monogenic Autoinflammatory Diseases

  2. Polygenic Autoinflammatory Diseases

Editors and Affiliations

  • New York University School of Medicine, New York, USA

    Petros Efthimiou

About the editor

Petros Efthimiou, MD

Clinical Professor of Medicine

New York University School of Medicine

New York, NY

Bibliographic Information

  • Book Title: Auto-Inflammatory Syndromes

  • Book Subtitle: Pathophysiology, Diagnosis, and Management

  • Editors: Petros Efthimiou

  • DOI:

  • Publisher: Springer Cham

  • eBook Packages: Medicine, Medicine (R0)

  • Copyright Information: Springer Nature Switzerland AG 2019

  • Hardcover ISBN: 978-3-319-96928-2Published: 17 January 2019

  • eBook ISBN: 978-3-319-96929-9Published: 04 January 2019

  • Edition Number: 1

  • Number of Pages: XIX, 322

  • Number of Illustrations: 8 b/w illustrations, 31 illustrations in colour

  • Topics: Rheumatology, Immunology

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