Fibrocystic Diseases of the Liver

  • Karen F. Murray
  • Anne M. Larson

Part of the Clinical Gastroenterology book series (CG)

Table of contents

  1. Front Matter
    Pages i-xiv
  2. Pathophysiology and Development

    1. Front Matter
      Pages 2-2
    2. Clifford W. Bogue
      Pages 3-21
    3. Silvia Lecchi, Luca Fabris, Carlo Spirli, Massimiliano Cadamuro, Romina Fiorotto, Mario Strazzabosco
      Pages 23-43
    4. Tatyana V. Masyuk, Anatoliy I. Masyuk, Nicholas F. LaRusso
      Pages 45-70
    5. Maya Tuchman, William A. Gahl, Meral Gunay-Aygun
      Pages 71-102
  3. Diagnosis

    1. Front Matter
      Pages 104-104
    2. Orpheus Kolokythas, Grace Phillips
      Pages 105-132
    3. Camtu D. Nguyen Truong, Matthew M. Yeh
      Pages 133-155
  4. Disease States

    1. Front Matter
      Pages 158-158
    2. Binita M. Kamath, Kathleen M. Loomes, David A. Piccoli
      Pages 159-178
    3. Ronald J. Sokol, Cara L. Mack
      Pages 179-199
    4. David A. Myers, Jordan M. Symons
      Pages 201-220
    5. Melissa A. Parisi, Laura S. Finn, Ian A. Glass
      Pages 221-256
    6. Aoife M. Waters, Philip L. Beales
      Pages 257-285
    7. Erik A. Eklund, Hudson H. Freeze
      Pages 287-317
    8. Jodi M. Smith, Ruth A. McDonald
      Pages 319-330
    9. Ronen Arnon, Henrietta Kotlus Rosenberg, Frederick J. Suchy
      Pages 331-358
    10. André A. S. Dick, Patrick J. Healey
      Pages 359-369
    11. Qi Qian, Vicente E. Torres, Stefan Somlo
      Pages 371-386

About this book

Introduction

In recent years there have been huge advances in the understanding of the genetic and molecular basis of the fibrocystic diseases. This volume provides a thorough review of fibrocyctic diseases that affect the liver. It contains in-depth discussions of the genetics, molecular biology, pathogenesis, histology, clinical presentations, complications of, treatment, and prognosis of the conditions affecting children and adults, and hence will be the gold-standard reference for these conditions. In addition, the histological features that distinguish these conditions from other potentially fibrosing hepatopathies are illustrated. Conditions with syndromic features involving the kidney or other organ systems are also reviewed. Thorough review of the clinical phenotypes, their presentations, treatment, potential complications of, and prognosis is discussed. Fibrocystic Diseases of the Liver will be an invaluable resource for hepatologists, gastroenterologists, nephrologists, and hepatic surgeons who care for children and adults with liver disease, as well as basic scientists in molecular genetics, hepatobiliary pathophysiology, hepatology and nephrology.

Keywords

Cholangiocyte Cystadenoma Fibrocystic Hepatic Cyst Joubert Syndrome Kidney Disease gastroenterology hepatology kidney liver liver disease nephrology pathophysiology physiology

Editors and affiliations

  • Karen F. Murray
    • 1
  • Anne M. Larson
    • 2
  1. 1.School of Medicine, Children's Hospital & RegionalUniversity of WashingtonSeattleUSA
  2. 2.St. Paul University HospitalDallasUSA

Bibliographic information

  • DOI https://doi.org/10.1007/978-1-60327-524-8
  • Copyright Information Springer Science+Business Media, LLC 2010
  • Publisher Name Humana Press
  • eBook Packages Medicine
  • Print ISBN 978-1-60327-523-1
  • Online ISBN 978-1-60327-524-8
  • About this book