Table of contents

  1. Front Matter
    Pages i-xiv
  2. Current Perspectives

  3. Basic Science Aspects

    1. Front Matter
      Pages 17-17
    2. Elke Voges, Annemarie Kronberger, Rosalind A. Grymes, Eugene A. Bauer
      Pages 63-69
    3. Ervin H. Epstein Jr.
      Pages 70-74
    4. David T. Woodley, W. Ray Gammon, Robert A. Briggaman
      Pages 75-86
  4. Clinical Overview

    1. Front Matter
      Pages 87-87
    2. Andrew N. Lin, D. Martin Carter
      Pages 89-117
    3. Andrew N. Lin, D. Martin Carter
      Pages 118-134
    4. Andrew N. Lin, D. Martin Carter
      Pages 152-165
  5. Extracutaneous Manifestations and Their Management

    1. Front Matter
      Pages 167-167
    2. Gulchin Ergun, Robert A. Schaefer
      Pages 169-184
    3. Patricia J. Giardina, Andrew N. Lin
      Pages 191-197
    4. John J. Putnam, George. W. Sferra Jr.
      Pages 198-209
    5. Andrew N. Lin, Shelley R. Berson, Robert F. Ward
      Pages 210-216
    6. Thomas J. A. Lehman
      Pages 217-219
  6. Special Management Considerations

    1. Front Matter
      Pages 221-221
    2. Kenneth O. Rothaus, Michael J. Pagnani
      Pages 223-227
    3. Robert E. Kelly
      Pages 228-234
    4. Virginia P. Sybert, Karen A. Holbrook
      Pages 235-251
    5. Rebecca L. Lipnick, Barbara S. Stanerson
      Pages 252-260
    6. Donna Tesi, Andrew N. Lin
      Pages 261-266
    7. Andrew N. Lin, D. Martin Carter
      Pages 267-280
    8. Dorothea Caldwell-Brown, Sheila Gibbons, Migdalia Reid
      Pages 281-294
  7. Back Matter
    Pages 295-302

About this book


Because skin blisters are the initial manifestation of epidermolysis bullosa (EB), patients invariably present to the dermatologist for diagnosis and treatment. However, EB is a systemic disease whose management requires input from clinicians in virtually all fields of medicine, including pediatri­ cians, surgeons, dentists, gastroenterologists, hematologists, otorhinolaryn­ gologists, dietitians, and physical therapists, to name a few. Because EB is a rare disease, few clinicians are familiar with it, and many recoil at the pros­ pect of caring for individuals covered with blisters caused by a disease they know little about. For patients, insult is thus added to injury and they feel abandoned, neglected, and frustrated. One way to remedy this deplorable situation is to provide clinicians with a compact source of information de­ tailing the principles of EB diagnosis and treatment. This text seeks to fulfill this role. From 1986-1991, The Rockefeller University Hospital has been the co­ ordinating center of the National EB Registry. Supported by The National Institutes of Health, this Registry consists of four university centers* commit­ ted to collecting clinical data concerning diagnosis, treatment, and epidemio­ logy on all American EB patients. As of April 1992, nearly 1,799 EB patients have enrolled nationwide. The Registry is now in its second five-year phase of operation.


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Editors and affiliations

  • Andrew N. Lin
    • 1
  • D. Martin Carter
    • 1
  1. 1.Laboratory for Investigative DermatologyThe Rockefeller UniversityNew YorkUSA

Bibliographic information