Prolonged peripheral facial nerve paralysis in a child -think of temporal bone rhabdomyosarcoma: case report
- 56 Downloads
Rhabdomyosarcoma is the most common type of soft tissue sarcoma in childhood. When localized in the middle ear and temporal bone, they are highly aggressive, whereas the outcome directly depends on an accurate and timely diagnosis, stage of the disease, and adequate multimodal therapy. Early clinical diagnosis of the temporal bone rhabdomyosarcoma is often difficult since clinical signs are not specific for this disease. We present a case of an embryonal rhabdomyosarcoma, botryoid subtype, of the middle ear in a girl aged 4 years and 4 months, diagnosed 34 days after the first symptoms — right ear pain with peripheral facial nerve palsy on the same side. The overall symptoms were poor, in no way suggesting such a serious condition. After the treatment, control follow-ups for more than 3 years showed no recurrence of the disease, while signs of the right peripheral facial palsy persist. Conclusion: In cases of prolonged peripheral facial nerve palsy in children, not responding to conservative treatment, a temporal bone rhabdomyosarcoma should be considered in a differential diagnosis.
KeywordsRhabdomyosarcoma Temporal bone Child
Unable to display preview. Download preview PDF.
- Akbar A, Sohail A. Rhabdomyosarcoma of the middle ear and mastoid: A case report and review of the literature. ENT J 2005:780–4Google Scholar
- Cotton RT, Rothschild MA, Zwerdling T. Tumors of the head and neck in children. In: Thawley SE, Panje WR, Batsakis JG, Lindberg RD, eds. Comprehensive Management of Head and Neck Tumors. 2nd ed. Philadelphia: W.B.Saunders. 1998:1846–902Google Scholar
- Adrassy R. Rhabdomyosarcoma. J Semin Pediatr Surg 1997;6:17–23Google Scholar
- Maurer HM. Rhabdomyosarcoma. Paediatr Ann 1979;8:35–48Google Scholar