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Perianal alveolar soft-part sarcoma: a rare case

  • Case Report
  • Published:
Central European Journal of Medicine

Abstract

Background

Alveolar soft part sarcoma (ASPS) is a rare diagnosis in the perianal region.

Methods

we describe the clinical presentation, pathological findings and differential diagnosis of a rare case of perianal ASPS. We also describe the importance of the preoperative embolization of the hypervascularised masses to prevent surgical bleeding.

Conclusions

clinical and pathological findings are essential for the diagnosis, specifically by immunochemistry and molecular techniques, as the demonstration of ASPL/TFE3 fusion transcript became indispensable in some cases. Preoperative embolization of the hypervascularised masses may prevent uncontrollable surgical bleeding.

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Author information

Authors and Affiliations

  1. Servicio de Cirugía General, Hospital Comarcal Valle de los Pedroches, 14400, Córdoba, Spain

    Jaime Alonso-Gómez

  2. Servicio de Anatomía Patológica, Hospital Universitario Reina Sofía, 14400, Córdoba, Spain

    María Teresa Caro-Cuenca

  3. Servicio de Cirugía General, Hospital Universitario Reina Sofía, 14400, Córdoba, Spain

    Antonio Membrives-Obrero, Rosa Ortega-Salas, José María Gallardo-Valverde, Rafael Orti-Rodríguez & Sebastián Rufián Peña

Authors
  1. Jaime Alonso-Gómez
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  2. María Teresa Caro-Cuenca
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  3. Antonio Membrives-Obrero
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  4. Rosa Ortega-Salas
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  5. José María Gallardo-Valverde
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  6. Rafael Orti-Rodríguez
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  7. Sebastián Rufián Peña
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Corresponding author

Correspondence to Jaime Alonso-Gómez.

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Alonso-Gómez, J., Caro-Cuenca, M.T., Membrives-Obrero, A. et al. Perianal alveolar soft-part sarcoma: a rare case. cent.eur.j.med 9, 246–249 (2014). https://doi.org/10.2478/s11536-012-0145-2

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  • DOI: https://doi.org/10.2478/s11536-012-0145-2

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