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Keratosis Follicularis Spinulosa Decalvans Associated with Acne Keloidalis Nuchae and Tufted Hair Folliculitis

  • Case Report
  • KFSD with Acne Keloidalis Nuchae
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Abstract

Keratosis follicularis spinulosa decalvans is a rare, X-linked disorder characterized by scarring alopecia of the scalp and eyebrows in the setting of widespread keratosis pilaris. Less frequent associations are ocular abnormalities and palmoplantar keratoderma. Acne keloidalis nuchae has previously been described in one patient with keratosis follicularis spinulosa decalvans. We report another case of keratosis follicularis spinulosa decalvans with acne keloidalis nuchae and tufted hair folliculitis, thus further establishing this association.

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Acknowledgments

No sources of funding were used to assist in the preparation of this case report. The authors have no conflicts of interest that are directly relevant to the content of this case report.

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Authors and Affiliations

  1. Ayza Skin & Research Center, Lalamusa, Pakistan

    Shahbaz A. Janjua (Dermatologist)

  2. Military Hospital, Rawalpindi, Pakistan

    Nadia Iftikhar

  3. Department of Dermatology and Venereology, Zagreb University Hospital Centre, Zagreb, Croatia

    Zrinjka Pastar

  4. Departments of Dermatology and Pathology, University of Texas Southwestern Medical Center, Dallas, Texas, USA

    Gregory A. Hosler

Authors
  1. Shahbaz A. Janjua
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  2. Nadia Iftikhar
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  3. Zrinjka Pastar
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  4. Gregory A. Hosler
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Corresponding author

Correspondence to Shahbaz A. Janjua.

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Janjua, S.A., Iftikhar, N., Pastar, Z. et al. Keratosis Follicularis Spinulosa Decalvans Associated with Acne Keloidalis Nuchae and Tufted Hair Folliculitis. Am J Clin Dermatol 9, 137–140 (2008). https://doi.org/10.2165/00128071-200809020-00009

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  • DOI: https://doi.org/10.2165/00128071-200809020-00009

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