International Journal of Hematology

, Volume 82, Issue 4, pp 338–342 | Cite as

Primary Tracheal Lymphoma: Case Report and Literature Review

  • Akiyoshi Takami
  • Hirokazu Okumura
  • Yoshinobu Maeda
  • Yoshihisa Kumano
  • Hidesaku Asakura
  • Makoto Oda
  • Kenji Omura
  • Shinji Nakao


We describe a 20-year-old Japanese woman with anaplastic large cell lymphoma in whom primary tracheal involvement was associated with life-threatening airway obstruction. After debulking surgery, the patient was successfully treated with chemotherapy and radiotherapy. A total of 28 cases of primary tracheal lymphoma were reviewed. Common clinical features included predominance of localized disease, respiratory symptoms resembling acute asthma, absence of hemoptysis, and rapid progression of tracheal stenosis. Various histological subtypes of primary tracheal lymphoma exist and are likely to determine prognosis.

Key words

Non-Hodgkin’s lymphoma Trachea Tracheal stenosis Extranodal Anaplastic large cell lymphoma 


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Copyright information

© The Japanese Society of Hematology 2005

Authors and Affiliations

  • Akiyoshi Takami
    • 1
  • Hirokazu Okumura
    • 1
  • Yoshinobu Maeda
    • 3
  • Yoshihisa Kumano
    • 1
  • Hidesaku Asakura
    • 1
  • Makoto Oda
    • 2
  • Kenji Omura
    • 2
  • Shinji Nakao
    • 1
  1. 1.Departments of Cellular Transplantation BiologyKanazawa University Graduate School of MedicineKanazawaJapan
  2. 2.General and Cardiothoracic SurgeryKanazawa University Graduate School of MedicineKanazawa
  3. 3.Department of PathologyToyama Red Cross HospitalToyamaJapan

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