Abstract
Background A 25-year-old woman presented with a history of abdominal pain. Endoscopy of the upper gastrointestinal tract revealed a tumor that protruded into the prepyloric antrum. After resection, a 'high-risk' gastrointestinal stromal tumor was histologically confirmed.
Investigations Endoscopy, endoscopic ultrasound, hemigastrectomy, [18F]-2-fluoro-2-deoxy-D-glucose (FDG)-PET/CT scan, histological examination, immunohistochemistry, cardiac MRI, high-resolution CT with electrocardiogram gating, CT angiography, and cardiac surgery.
Diagnosis Gastrointestinal stromal tumor, epicardial paraganglioma, and Carney's syndrome.
Management Abdominal ultrasound and endoscopy combined with endoscopic ultrasound, annual FDG-PET/CT scan.
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V Kächele and S Pauls contributed equally to this work.
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Kächele, V., Pauls, S., Mottaghy, F. et al. A 25-year-old woman with a gastric GIST and a PET-positive epicardial tumor. Nat Rev Clin Oncol 4, 197–201 (2007). https://doi.org/10.1038/ncponc0743
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DOI: https://doi.org/10.1038/ncponc0743
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