Abstract
von Hippel-Lindau (VHL) disease is an autosomaldominant disorder characterized by cysts andcystadenoma in the kidney, pancreas andepididymis and angiomas of the central nervoussystem and retina as well as renal cellcarcinoma (RCC), phaeochromocytoma, islettumors of the pancreas, and endolympatic sactumors. VHL for its multicentric-characteristicand bilateralism often puts the surgeon inchallenging situation. We present a case of VHLwith bilateral RCC and retinal angiomas managedwith right radical nephrectomy and left repeatpartial nephrectomy.
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Ansari, M., Gupta, N. & Kumar, P. von Hippel-Lindau disease with bilateral multiple renal cell carcinoma managed by right radical nephrectomy and left repeat partial nephrectomy. Int Urol Nephrol 35, 471–473 (2003). https://doi.org/10.1023/B:UROL.0000025633.40416.57
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DOI: https://doi.org/10.1023/B:UROL.0000025633.40416.57