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Propionic acidaemia with basal ganglia stroke: Treatment of acute extrapyramidal symptoms with L-DOPA

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Journal of Inherited Metabolic Disease

Abstract

A 15-year-old male with propionic acidaemia developed neurological complications secondary to basal ganglia involvement. Treatment with L-DOPA had a positive effect on his extrapyramidal syndrome.

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Authors and Affiliations

  1. Department of Neurological and Psychiatric Sciences, University of Padua, Padua, Italy

    A. P. Burlina & C. Baracchini

  2. Division of Neuroradiology, Azienda Ospedaliera of Padua, Padua, Italy

    C. Carollo

  3. Department of Pediatrics, University of Padua, Padua, Italy

    A. B. Burlina

Authors
  1. A. P. Burlina
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  2. C. Baracchini
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  3. C. Carollo
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  4. A. B. Burlina
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Burlina, A.P., Baracchini, C., Carollo, C. et al. Propionic acidaemia with basal ganglia stroke: Treatment of acute extrapyramidal symptoms with L-DOPA. J Inherit Metab Dis 24, 596–598 (2001). https://doi.org/10.1023/A:1012471928628

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  • DOI: https://doi.org/10.1023/A:1012471928628

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