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Giant angiomyolipoma associated with marked pulmonary lesions suggesting lymphangioleiomyomatosis in a patient with tuberous sclerosis

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Abstract

The association between Tuberous Sclerosis (TS) and Angiomyolipoma (AML) is well known. A patient with TS and giant AML mimicking Renal Cell Carcinoma (RCC), measuring 29 × 18 × 11 cm, weighing 4700 gr is presented. Imaging studies revealed coexistent pulmonary lymphangioleiomyomatosis and concurrent renal and pulmonary involvement is extremely rare in patients in TS. We believe that the growth potential of this hamartomatous lesion may reach to a life threatening size.

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Authors and Affiliations

  1. Department of Urology, Dokuz Eylül University, School of Medicine, İnciraltı, İzmir, Turkey

    E. Tüzel, Z. Kırkalı, U. Mungan, C. Cüler & M. Sade

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  1. E. Tüzel
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  2. Z. Kırkalı
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  3. U. Mungan
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  4. C. Cüler
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  5. M. Sade
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Tüzel, E., Kırkalı, Z., Mungan, U. et al. Giant angiomyolipoma associated with marked pulmonary lesions suggesting lymphangioleiomyomatosis in a patient with tuberous sclerosis. Int Urol Nephrol 32, 219–222 (2000). https://doi.org/10.1023/A:1007183001681

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  • DOI: https://doi.org/10.1023/A:1007183001681

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