European Journal of Epidemiology

, Volume 18, Issue 6, pp 473–477

REVIEW: Variant Creutzfeldt-Jakob disease

  • Esther A. Croes
  • Cornelia M. van Duijn


A variant form of Creutzfeldt-Jakob disease (vCJD) has had major impact in Europe during the last decade. In this article, we review the aetiology of vCJD and its relation with bovine spongiform encephalopathy. Further, treatment of the disease, the strategies focusing on prevention of transmission, future prospects, and the limitations encountered in epidemiological research of vCJD are discussed.


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Copyright information

© Kluwer Academic Publishers 2003

Authors and Affiliations

  • Esther A. Croes
    • 1
  • Cornelia M. van Duijn
    • 1
  1. 1.Genetic Epidemiology Unit, Department of Epidemiology and BiostatisticsErasmus MCRotterdamThe Netherlands

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