Bilateral Sprengel’s Deformity Treated with the Modified Woodward Procedure: Technique and Outcome of 3 Consecutive Case Reports

Abstract

Sprengel’s deformity is a congenital anomaly characterized by a hypoplastic and elevated scapula that results in cosmetic and functional impairment. In this study, we report the results of 3 severe cases of bilateral Sprengel’s deformity with associated Klippel-Feil syndrome treated by the modified Woodward procedure. Between 2013 and 2015, 3 patients of a mean age of 5.4 years were diagnosed with bilateral Sprengel’s deformity and associated Klippel-Feil syndrome. All the shoulders were graded as Cavendish 4 and had a bar connecting the scapula with the cervical vertebrae. Patients were managed surgically with the modified Woodward procedure and a clavicular osteotomy. The mean follow-up time was 62 months. No intraoperative or postoperative complications were recorded and all patients remained neurologically intact. The average improvement of the abduction of the shoulders was 30° and the mean lowering of the scapula was 2.6 cm. All patients improved by at least 1 Cavendish grade. The modified Woodward procedure is a reliable and effective technique to improve shoulder cosmesis and function even in severe cases of bilateral Sprengel’s deformity with associated Klippel-Feil syndrome.

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Availability of Data and Material

The data that support the findings of this study are available from the corresponding author (Frideriki Poutoglidou) upon reasonable request.

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Frideriki Poutoglidou assisted with the surgical operations, collected the data, drafted the manuscript, provided final approval of the version to be published, and has agreed to be accountable for all the aspects of the work in ensuring that questions related to the accuracy or integrity of any part of the work are appropriately investigated and resolved.

Dimitrios Metaxiotis performed the surgical procedures, drafted the manuscript, and provided final approval of the version to be published.

Dimitrios Alvanos assisted with the surgical operations, helped shape the final manuscript, and provided final approval of the version to be published.

Anastasios Mpeletsiotis participated in the drafting of the manuscript and provided critical feedback and final approval of the version to be published.

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Correspondence to Frideriki Poutoglidou.

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This retrospective study was approved by our hospital’s Institutional Review Board.

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Poutoglidou, F., Metaxiotis, D., Alvanos, D. et al. Bilateral Sprengel’s Deformity Treated with the Modified Woodward Procedure: Technique and Outcome of 3 Consecutive Case Reports. SN Compr. Clin. Med. 3, 754–758 (2021). https://doi.org/10.1007/s42399-021-00781-y

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Keywords

  • Sprengel’s deformity
  • Klippel-Feil syndrome
  • Woodward procedure
  • Congenital disorder
  • Shoulder