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Difficulty eating and significant weight loss in joint hypermobility syndrome/Ehlers–Danlos syndrome, hypermobility type

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Abstract

Joint Hypermobility Syndrome, also known as Ehlers–Danlos Syndrome Hypermobility Type (JHS/EDS-HT), is a heritable disorder of connective tissue, common but poorly known by the medical community. Although generalized joint hypermobility and fragility of tissues have been described as core features, recent research highlights the multisystemic nature of JHS/EDS-HT, which presents with a wide range of articular and extra-articular symptoms. Among these, gastrointestinal problems, temporomandibular disorders, and smell and taste abnormalities are common among those affected, having significant implications for eating. The present work reviews the literature linking JHS/EDS-HT and eating problems. Two illustrative case reports, in which JHS/EDS-HT manifestations contribute to developing and maintaining disturbed eating behaviors and significant weight loss, are presented.

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Authors and Affiliations

  1. Institut de Psychologie, Université Paris Descartes, Sorbonne Paris Cité, 71 Avenue Edouard Vaillant, 92100, Boulogne-Billancourt Cedex, France

    Carolina Baeza-Velasco

  2. Centre de Réadaptation Fonctionnelle, CHU de Toulouse, Toulouse, France

    Thomas Van den Bossche

  3. Consultation Ehlers-Danlos, Centre de Diagnostic et de Thérapeutique, Hôtel-Dieu, Paris, France

    Daniel Grossin & Claude Hamonet

  4. Faculté de Médecine, Université Paris-Est-Créteil, Créteil, France

    Claude Hamonet

Authors
  1. Carolina Baeza-Velasco
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  2. Thomas Van den Bossche
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  3. Daniel Grossin
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  4. Claude Hamonet
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Correspondence to Carolina Baeza-Velasco.

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The study was conducted according to the ethical principles of the Helsinki Declaration of 1964, revised in 2004, and in agreement with local ethics requirements.

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An informed consent was obtained from all participants before entering the study.

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Baeza-Velasco, C., Van den Bossche, T., Grossin, D. et al. Difficulty eating and significant weight loss in joint hypermobility syndrome/Ehlers–Danlos syndrome, hypermobility type. Eat Weight Disord 21, 175–183 (2016). https://doi.org/10.1007/s40519-015-0232-x

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