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Anesthesia for Long QT Syndrome

  • Pediatric Anesthesia (R Agarwal, Section Editor)
  • Published:
Current Anesthesiology Reports Aims and scope Submit manuscript

Abstract

Purpose of Review

This review article seeks to discuss the salient information about the known genetic variants associated with congenital long QT syndrome (LQTS) and describe the current anesthetic considerations.

Recent Findings

LQTS describes a heterogeneous group of patients with varying genetic mutations that cause an increased risk of torsade de pointe and sudden death. Research continues to identify more genetic mutations associated with LQTS subtypes. Publications of clinical experience with LQTS patients under general anesthesia provide new insights on the risk of medication inducing arrhythmias in these patients.

Summary

Many medications used during general anesthesia are known to prolong the QTc interval. Patients with LQTS are at increased risk of arrhythmias under general anesthesia.

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Papers of particular interest, published recently, have been highlighted as: • Of importance

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Authors and Affiliations

  1. Department of Anesthesiology, Perioperative and Pain Medicine, Stanford University School of Medicine, Stanford, USA

    Amy Babb & Julianne Mendoza

  2. Division of Pediatric Anesthesia, Lucile Packard Children’s Hospital, Stanford University School of Medicine, 300 Pasteur Dr, Stanford, CA, 94305, USA

    Amy Babb & Julianne Mendoza

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  1. Amy Babb
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Correspondence to Amy Babb.

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This article is part of theTopical Collection on Pediatric Anesthesia

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Babb, A., Mendoza, J. Anesthesia for Long QT Syndrome. Curr Anesthesiol Rep 11, 483–489 (2021). https://doi.org/10.1007/s40140-021-00480-3

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  • DOI: https://doi.org/10.1007/s40140-021-00480-3

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