Abstract
Osteogenesis imperfecta (OI) is a predominantly autosomal dominant inherited condition involving connective tissue associated with not only bone fragility, but multi-system involvement with perioperative implications. The perioperative management of patients with OI undergoing orthopedic procedures is high risk for anatomical and physiological reasons. We performed a retrospective analysis of 13 years of data covering the perioperative management of 146 pediatric patients with OI for 280 operative procedures involving up to five bones each by two fellowship-trained pediatric orthopedic surgeons and a team of pediatric anesthesiologists. The purpose of the review was to describe updated perioperative anesthetic management based on over a decade of experience in a pediatric hospital specializing in the management of OI patients.
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Jessica K. Goeller, Cynthia A. Ferris, Paul W. Esposito, Maegen J. Wallace, Bridget A. Burke, and Cynthia R. Bailey declare they have no conflict of interest.
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Goeller, J.K., Esposito, P.W., Wallace, M.J. et al. Perioperative Management of Pediatric Patients with Osteogenesis Imperfecta Undergoing Orthopedic Procedures. Curr Anesthesiol Rep 7, 142–149 (2017). https://doi.org/10.1007/s40140-017-0207-8
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DOI: https://doi.org/10.1007/s40140-017-0207-8