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Hypokalemic periodic paralysis and distal renal tubular acidosis associated with renal morphological changes

Abstract

We report an unusual case of 5-yrs-old girl presenting with recurrent episodic weakness with documented hypokalemia, polyuria and failure to thrive. The child was finally diagnosed as having distal renal tubular acidosis. Imaging studies revealed associated hypoechoic spaces in renal medulla. Long term treatment with alkali and maintenance of normokalemia lead to regression of these morphological changes.

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Correspondence to Ratan Gupta.

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Gupta, R., Saurabh, K., Sharma, S. et al. Hypokalemic periodic paralysis and distal renal tubular acidosis associated with renal morphological changes. Indian Pediatr 50, 336–337 (2013). https://doi.org/10.1007/s13312-013-0072-6

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  • DOI: https://doi.org/10.1007/s13312-013-0072-6

Key words

  • Hypoechoeic medullary spaces
  • Hypokalemic periodic paralysis
  • Renal tubular acidosis (RTA)