Abstract
Mesenteric fibromatosis is a benign fibrous tumor, characterized by proliferations of fibroblasts and myofibroblasts, locally aggressive but non-metastasizing. It can occur rarely in association with familial adenomatous polyposis or sporadically (related with previous trauma, abdominal surgery or prolonged estrogens intake). Small bowel mesentery is the most common site of origin of mesenteric fibromatosis. The authors report a case of a 47-years-old male with a large mass involving the mesentery of the first jejunal loops. The patient was symptomatic for nausea and referred an increasing abdominal circumference; a CT scan showed a huge mass (34 × 29 × 15 cm) very close to the superior mesenteric vessel roots. The surgical treatment consisted in the en bloc removal of the mass weighting 13 kg.
References
Burke AP, Sobin LH, Shekitka KM, Federspiel BH, Helwig EB (1990) Intra-abdominal fibromatosis. A pathologic analysis of 130 tumors with comparison of clinical subgroups. Am J Surg Pathol 14(4):335–341
Levy AD, Rimola J, Mehrotra AK, Sobin LH (2006) From the archives of the AFIP: benign fibrous tumors and tumorlike lesions of the mesentery: radiologic–pathologic correlation. Radiographics 26(1):245–264
Smith AJ, Lewis JJ, Merchant NB, Leung DH, Woodruff JM, Brennan MF (2000) Surgical management of intra-abdominal desmoid tumours. Br J Surg 87(5):608–613
Lazar AJ, Tuvin D, Hajibashi S, Habeeb S, Bolshakov S, Mayordomo-Aranda E et al (2008) Specific mutations in the beta-catenin gene (CTNNB1) correlate with local recurrence in sporadic desmoid tumors. Am J Pathol 173(5):1518–1527
Domont J, Salas S, Lacroix L, Brouste V, Saulnier P, Terrier P et al (2010) High frequency of beta-catenin heterozygous mutations in extra-abdominal fibromatosis: a potential molecular tool for disease management. Br J Cancer 102(6):1032–1036
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Menegazzo, M., Tonello, M. & Bardini, R. A 13 kg intra-abdominal mass: a case of mesenteric fibromatosis. Updates Surg 65, 237–240 (2013). https://doi.org/10.1007/s13304-012-0143-6
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DOI: https://doi.org/10.1007/s13304-012-0143-6