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Fibrosarcomatous dermatofibrosarcoma metastasizing to retroperitoneum four years after resection of primary lesion - A case report with review of literature

  • Case Report
  • Published:
Hellenic Journal of Surgery

Abstract

Dermatofibrosarcoma protuberans (DFSP) is a rare soft tissue neoplasm arising from mesenchymal cells, making up about 6% of all soft tissue tumours1. The most commonly involved sites are the trunk (42–72%) and proximal extremities (16–30%)2. It generally has intermediate- to low-grade malignancy potential with the exception of the fibrosarcomatous variant (high-grade). This variant is more likely to metastasise (in less than 5% of cases) to the lungs and lymph nodes and may occur many years after the onset of disease3. Herein, we present the case of a 40-yearold male who presented with a two-month history of a lump in the upper abdomen with pressure symptoms and past history of recurrent dermatofibrosarcoma of the left shoulder. Computed tomography (CT) revealed a mass arising from the greater curvature of the stomach. The patient underwent exploratory laparotomy which revealed a tumour mass arising from the retroperitoneum The mass was resected and sent for histopathology which revealed a fibrosarcomatous variant of dermatofibrosarcoma protuberans (FS-DFSP).

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Authors and Affiliations

  1. Department of Surgery, PGIMER and Dr RML Hospital, Delhi, India

    Nikhil Gupta, Umesh Krishnegowda, Dipankar Naskar & C.K. Durga

  2. Department of Surgery, Dr RML Hospital, Delhi, India

    Arun K. Gupta

  3. Department of Pathology, Dr RML Hospital, Delhi, India

    Meenakshi Bhardwaj

Authors
  1. Nikhil Gupta
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  2. Arun K. Gupta
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  3. Umesh Krishnegowda
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  4. Meenakshi Bhardwaj
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  5. Dipankar Naskar
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  6. C.K. Durga
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Correspondence to Nikhil Gupta.

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Gupta, N., Gupta, A.K., Krishnegowda, U. et al. Fibrosarcomatous dermatofibrosarcoma metastasizing to retroperitoneum four years after resection of primary lesion - A case report with review of literature. Hellenic J Surg 87, 505–508 (2015). https://doi.org/10.1007/s13126-015-0270-x

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  • DOI: https://doi.org/10.1007/s13126-015-0270-x

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