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Hellenic Journal of Surgery

, Volume 86, Issue 3, pp 155–158 | Cite as

Syringocystadenoma papilliferum on the breast: An unusual location

  • Arghya BasuEmail author
  • Dawood Khan
  • Sukumar Maiti
  • Soumika Biswas
Case Report
  • 34 Downloads

Abstract

Introduction

Syringocystadenoma papilliferum (SCAP), otherwise known as naevus syringocystadenomatosus papilliferus, is a skin hamartoma originating from apocrine or exocrine sweat glands [1], microscopically characterized by papillary invaginations lined by bi-layered epithelium and decapitation secretion rich in plasmacytes [3].

Case Report

A 29-year-old female presented with a cluster of large fleshy, irregular, sessile, moist, pinkish tumours located over her left breast, with pain, itching, discharge and bleeding upon friction with undergarments.

Discussion

SCAP is an uncommon skin tumour usually seen in children or adolescents as a firm plaque of skincoloured to pinkish-brown hairless grouped nodules or a solitary nodule. Verrucous, papillary, hyperkeratotic, fleshy transformations are often seen in puberty [4,5]. Uncommon sites, such as the buttock, vulva, scrotum, pinna, eyelid, outer ear canal, postoperative scar, thigh, axilla, arms, lower limb, inguinal and perineal regions, have also been reported [6–9].

Conclusion

SCAP is a rare adnexal tumour commonly arising in association with congenital Sebaceous Naevus of Jadassohn. A watchful alertness is mandatory as adulthood malignancies can occur in more than one-third of this deceptively docile tumour.

Key words

Syringocystadenomatosus papilliferus breast tumour hamartoma 

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Copyright information

© Hellenic Surgical Society and Springer-Verlag Wien 2014

Authors and Affiliations

  • Arghya Basu
    • 1
    • 3
    Email author
  • Dawood Khan
    • 1
  • Sukumar Maiti
    • 1
  • Soumika Biswas
    • 2
  1. 1.Department of General SurgeryMedical College and HospitalKolkataIndia
  2. 2.Department of BiochemistryMedical College and HospitalKolkataIndia
  3. 3.West BengalIndia

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