Abstract
IgG4-related disease (IgG4 RD) is a multisystem disorder characterized by tumefactive (mass forming) lesions, storiform fibrosis, and IgG4-positive plasma cell infiltration. IgG4 sclerosing cholangitis (IgG4 SC) is the biliary manifestation of IgG4 RD, often in association with autoimmune pancreatitis (AIP). Here, we report two patients with IgG4-related cholangitis mimicking primary sclerosing cholangitis.
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HKN, SJB, MKP, IC, and SCS declare that they have no conflict of interest.
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Nayak, H.K., Bhat, S.J., Panigrahi, M.K. et al. IgG4-related sclerosing cholangitis— A great mimicker. Indian J Gastroenterol 39, 614–618 (2020). https://doi.org/10.1007/s12664-020-01102-2
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DOI: https://doi.org/10.1007/s12664-020-01102-2