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Génitoplasties féminisantes

Feminizing genitoplasty

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Revue de médecine périnatale

Résumé

La complexité et la diversité des pathologies pouvant amener à proposer une génitoplastie féminisante demandent que ces enfants soient pris en charge dès la naissance par des équipes multidisciplinaires expérimentées. Un débat existe concernant les indications, le timing et le type de génitoplastie. Nous passons en revue les principales pathologies concernées et nous décrivons les principes des interventions actuelles. Nous rapportons également les résultats postopératoires de cette chirurgie.

Abstract

The complexity and diversity of pathologies in a feminizing genitoplasty, require a multidisciplinary management by an experienced team. There is an ongoing debate about the indications, timing, and type of feminizing genitoplasty in DSD patients. This article describes the various types of DSD patients, and also the current techniques and outcomes of feminizing surgery.

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Abbreviations

DSD:

disorders of sex development

OGE:

organes génitaux externes

OGI:

organes génitaux internes

HCS:

hyperplasie congénitale de surrénale

AIS:

insensibilité aux androgènes (CAIS = complète, PAIS = partielle)

DGM:

dysgénésie gonadique mixte

AMH:

hormone antimüllérien

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Authors and Affiliations

  1. Service de chirurgie pédiatrique, hospices civils de Lyon, groupe hospitalier Est, hôpital femme—mère—enfant, 59, boulevard Pinel, F-69677, Bron cedex, France

    D. -B. Gorduza

  2. Service de chirurgie pédiatrique, université Claude-Bernard, Lyon-I, hospices civils de Lyon, groupe hospitalier Est, hôpital femme—mère—enfant, 59, boulevard Pinel, F-69677, Bron cedex, France

    L. Margain-Deslandes, P. Mouriquand & P. -Y. Mure

Authors
  1. D. -B. Gorduza
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  2. L. Margain-Deslandes
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  3. P. Mouriquand
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  4. P. -Y. Mure
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Corresponding author

Correspondence to P. -Y. Mure.

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Gorduza, D.B., Margain-Deslandes, L., Mouriquand, P. et al. Génitoplasties féminisantes. Rev. med. perinat. 7, 161–170 (2015). https://doi.org/10.1007/s12611-015-0330-z

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  • DOI: https://doi.org/10.1007/s12611-015-0330-z

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