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Markedly dilated right atrium in an infant: what is the diagnosis?

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Abstract

An 18-month-old boy presented with recurrent episodes of irritability and documented fast heart rate suggestive of supraventricular tachycardia. Cardiovascular examination revealed significant cardiomegaly, normal heart sounds and no murmurs. The differential diagnosis of marked right atrial dilatation and management principles of idiopathic dilatation of the right atrium are described.

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All data supporting the findings of this case study are available within the paper and its Supplementary Information.

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All authors contributed equally to the preparation of the manuscript.

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Correspondence to Arun Gopalakrishnan.

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All procedures followed were in accordance with the ethical standards of the responsible committee on human experimentation (institutional and national) and with the Helsinki Declaration of 1964 and later revisions. Informed consent was obtained from the patient for being included in the study. No patient identity particulars have been disclosed.

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Video 1: Video 1 is the echocardiographic cine-loop from the apical four-chamber view showing idiopathic dilatation of the right atrium (MP4 1772 kb)

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Sambaturu, V.K., Sugathan, V., Sasikumar, D. et al. Markedly dilated right atrium in an infant: what is the diagnosis?. J Echocardiogr (2024). https://doi.org/10.1007/s12574-024-00651-1

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  • DOI: https://doi.org/10.1007/s12574-024-00651-1

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