Skip to main content

Advertisement

SpringerLink
Log in

Sclerosing PEComa: A histologic surprise

  • Case Report
  • Published:
African Journal of Urology Submit manuscript

Abstract

PEComa represents a group of mesenchymal tumors consisting of perivascular epithelioid cells. We present a 50-year old female patient with a rare distinctive variant, sclerosing PEComa, characterized by extensive stromal hyalinization and a predilection for the pararenal retroperitoneum.

This is a preview of subscription content, log in via an institution to check access.

Access this article

Log in via an institution

Price excludes VAT (USA)
Tax calculation will be finalised during checkout.

Instant access to the full article PDF.

Institutional subscriptions

Similar content being viewed by others

References

  1. Walsh SN, Sangüeza OP. PEComas: A review with emphasis on cutaneous lesions. Semin. Diagn. Pathol. 2009;26(3):123–130.

    Article  PubMed  Google Scholar 

  2. Hornick JL, Fletcher CDM. Sclerosing PEComa: Clinicopathologic analysis of a distinctive variant with a predilection for the retroperitoneum. Am. J. Surg.Pathol. 2008;32(4):493–501.

    Article  PubMed  Google Scholar 

  3. Bonetti F, Pea M, Martignoni G, Zamboni G, Gaffey MJ, Mills SE, et al. PEC and Sugar. Am.J.Surg.Pathol. 1992;16(3):307–308.

    Article  PubMed  CAS  Google Scholar 

  4. Folpe AL, Mentzel T, Lehr HA, Fisher C, Balzer BL, Weiss SW. Perivascular epithelioid cell neoplasms of soft tissue and gynecologic origin: A clinicopathologic study of 26 cases and review of the literature. Am.J.Surg.Pathol. 2005;29(12):1558–1575.

    Article  PubMed  Google Scholar 

  5. The International Agency for Research on Cancer, Eble J, Epstein J, Sesterhenn I, Sauter G. WHO classification of tumours: Pathology and genetics of tumours of the urinary system and male genital organs. 1st ed. International Agency for Research on Cancer; 2004.

  6. Armah HB, Parwani AV. Malignant perivascular epithelioid cell tumor (PEComa) of the uterus with late renal and pulmonary metastases: A case report with review of the literature. Diagn.Pathol. 2007; 2(1): Art. no. 45.

    Google Scholar 

  7. Enzinger FM, Weiss SW, Goldblum JR. Enzinger and Weiss’s soft tissue tumors. 5th ed. Mosby; 2007.

  8. Matsuyama A, Hisaoka M, Ichikawa K, Fujimori T, Udo K, Uchihashi K, et al. Sclerosing variant of epithelioid angiomyolipoma. Pathology International. 2008;58(5):306–310.

    Article  PubMed  Google Scholar 

  9. Martignoni G, Pea M, Reghellin D, Zamboni G, Bonetti F. PEComas: The past, the present and the future. Virchows Arch. 2008;452(2):119–132.

    Article  PubMed  Google Scholar 

Download references

Author information

Authors and Affiliations

  1. Kasturba Medical College and Hospital, Manipal University, Manipal, India

    Manna Valiathan, B. P. Sunil, L. Rao, V. Geetha & P. Hedge

  2. Department of Pathology, Kasturba Medical College, Manipal University, Manipal, 576104, Karnataka, India

    Manna Valiathan

Authors
  1. Manna Valiathan
    View author publications

    You can also search for this author in PubMed Google Scholar

  2. B. P. Sunil
    View author publications

    You can also search for this author in PubMed Google Scholar

  3. L. Rao
    View author publications

    You can also search for this author in PubMed Google Scholar

  4. V. Geetha
    View author publications

    You can also search for this author in PubMed Google Scholar

  5. P. Hedge
    View author publications

    You can also search for this author in PubMed Google Scholar

Corresponding author

Correspondence to Manna Valiathan.

About this article

Cite this article

Valiathan, M., Sunil, B.P., Rao, L. et al. Sclerosing PEComa: A histologic surprise. Afr J Urol 17, 97–100 (2011). https://doi.org/10.1007/s12301-011-0018-y

Download citation

  • Received:

  • Accepted:

  • Published:

  • Issue Date:

  • DOI: https://doi.org/10.1007/s12301-011-0018-y

Key Words

Search

Navigation